Anti-Fibrillin 1 Polyclonal Antibody, 100.0ul
£431.71
Delivery: 2 weeks
SKU
K009972P-100.0ul
This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12 nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosy
This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12 nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosynostosis syndrome. [provided by RefSeq, Jul 2008]
- Size: 100.0ul
- Molecular Weight: 316kDa
- Physical State: Liquid
- Storage: Store at -20℃. Avoid freeze / thaw cycles.
- Synonyms: fibrillin1, 350 kDa glycoprotein component extracellular microfibril, FBN 1, FBN1, FBN, Fibrillin 15, Fibrillin15, Marfan syndrome, MASS, MFS 1, MFS1, OCTD, SGS, Weill Marchesani syndrome, WMS, AI536462, B430209H23, Fib-1, Fibrilin-1, ACMICD, FBN1_HUMAN, GPHYSD2, SSKS, Weill Marchesani syndrome, WMS2
- Application: ELISA;IF;IHC
- Brand: Saint Michael
- Catalogue No.: K009972P-100.0ul
For laboratory research use only. Not for human or animal consumption, diagnostic or therapeutic use.
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